CLCN4 (chloride voltage-gated channel 4)

2007-04-01  

Identity

HGNC
LOCATION
Xp22.2
LOCUSID
ALIAS
CLC4,ClC-4,ClC-4A,MRX15,MRX49,MRXSRC
FUSION GENES

Other Information

Locus ID:

NCBI: 1183
MIM: 302910
HGNC: 2022
Ensembl: ENSG00000073464

Variants:

dbSNP: 1183
ClinVar: 1183
TCGA: ENSG00000073464
COSMIC: CLCN4

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000073464ENST00000380829G3XAG5
ENSG00000073464ENST00000380833P51793
ENSG00000073464ENST00000421085P51793
ENSG00000073464ENST00000454850E9PFB5

Expression (GTEx)

0
10
20
30
40
50
60

Pathways

PathwaySourceExternal ID
Transmembrane transport of small moleculesREACTOMER-HSA-382551
Ion channel transportREACTOMER-HSA-983712
Stimuli-sensing channelsREACTOMER-HSA-2672351

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
363851662023Functional and clinical studies reveal pathophysiological complexity of CLCN4-related neurodevelopmental condition.9
363851662023Functional and clinical studies reveal pathophysiological complexity of CLCN4-related neurodevelopmental condition.9
339511952021The molecular and phenotypic spectrum of CLCN4-related epilepsy.8
339511952021The molecular and phenotypic spectrum of CLCN4-related epilepsy.8
275508442018De novo and inherited mutations in the X-linked gene CLCN4 are associated with syndromic intellectual disability and behavior and seizure disorders in males and females.28
275508442018De novo and inherited mutations in the X-linked gene CLCN4 are associated with syndromic intellectual disability and behavior and seizure disorders in males and females.28
289721562017Preferential association with ClC-3 permits sorting of ClC-4 into endosomal compartments.13
289721562017Preferential association with ClC-3 permits sorting of ClC-4 into endosomal compartments.13
236470722013Exome sequencing reveals new causal mutations in children with epileptic encephalopathies.131
236470722013Exome sequencing reveals new causal mutations in children with epileptic encephalopathies.131
213543962011Anion- and proton-dependent gating of ClC-4 anion/proton transporter under uncoupling conditions.20
213543962011Anion- and proton-dependent gating of ClC-4 anion/proton transporter under uncoupling conditions.20
200873502010Gene trapping identifies chloride channel 4 as a novel inducer of colon cancer cell migration, invasion and metastases.6
200873502010Gene trapping identifies chloride channel 4 as a novel inducer of colon cancer cell migration, invasion and metastases.6
193648862009Channel-like slippage modes in the human anion/proton exchanger ClC-4.39

Citation

Dessen P

CLCN4 (chloride voltage-gated channel 4)

Atlas Genet Cytogenet Oncol Haematol. 2007-04-01

Online version: http://atlasgeneticsoncology.org/gene/46770/clcn4