GJB2 (gap junction protein beta 2)

2003-05-01  

Identity

HGNC
LOCATION
13q12.11
LOCUSID
ALIAS
BAPS,CX26,DFNA3,DFNA3A,DFNB1,DFNB1A,HID,KID,NSRD1,PPK

Other Information

Locus ID:

NCBI: 2706
MIM: 121011
HGNC: 4284
Ensembl: ENSG00000165474

Variants:

dbSNP: 2706
ClinVar: 2706
TCGA: ENSG00000165474
COSMIC: GJB2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000165474ENST00000382844P29033
ENSG00000165474ENST00000382844H9U1J4
ENSG00000165474ENST00000382848P29033
ENSG00000165474ENST00000382848H9U1J4

Expression (GTEx)

0
500
1000
1500

Pathways

PathwaySourceExternal ID
Vesicle-mediated transportREACTOMER-HSA-5653656
Membrane TraffickingREACTOMER-HSA-199991
Gap junction trafficking and regulationREACTOMER-HSA-157858
Gap junction traffickingREACTOMER-HSA-190828
Gap junction assemblyREACTOMER-HSA-190861
Transport of connexins along the secretory pathwayREACTOMER-HSA-190827
Oligomerization of connexins into connexonsREACTOMER-HSA-190704
Transport of connexons to the plasma membraneREACTOMER-HSA-190872

Protein levels (Protein atlas)

Not detected
Low
Medium
High

References

Pubmed IDYearTitleCitations
380295952024Mutation analysis of GJB2, SLC26A4, GJB3 and mtDNA12SrRNA genes in 251 non-syndromic hearing loss patients in Fujian, China.0
382128002024Interactions of genetic variations in FAS, GJB2 and PTPRN2 are associated with noise-induced hearing loss: a case-control study in China.0
382530332024Unraveling the Diversity of GJB2 Mutations in Nonsyndromic Hearing Loss: A Comprehensive Study in the Moroccan Population.0
384757712024Reconstructing the ancestral gene pool to uncover the origins and genetic links of Hmong-Mien speakers.0
387200482024Comparison of vestibular function in hereditary hearing loss patients with GJB2, CDH23, and SLC26A4 variants.0
387304442024Structural basis for pathogenic variants of GJB2 and hearing levels of patients with hearing loss.0
388290312024Structures of wild-type and a constitutively closed mutant of connexin26 shed light on channel regulation by CO(2).0
380295952024Mutation analysis of GJB2, SLC26A4, GJB3 and mtDNA12SrRNA genes in 251 non-syndromic hearing loss patients in Fujian, China.0
382128002024Interactions of genetic variations in FAS, GJB2 and PTPRN2 are associated with noise-induced hearing loss: a case-control study in China.0
382530332024Unraveling the Diversity of GJB2 Mutations in Nonsyndromic Hearing Loss: A Comprehensive Study in the Moroccan Population.0
384757712024Reconstructing the ancestral gene pool to uncover the origins and genetic links of Hmong-Mien speakers.0
387200482024Comparison of vestibular function in hereditary hearing loss patients with GJB2, CDH23, and SLC26A4 variants.0
387304442024Structural basis for pathogenic variants of GJB2 and hearing levels of patients with hearing loss.0
388290312024Structures of wild-type and a constitutively closed mutant of connexin26 shed light on channel regulation by CO(2).0
360482362023Comprehensive interpretation of single-nucleotide substitutions in GJB2 reveals the genetic and phenotypic landscape of GJB2-related hearing loss.4

Citation

Dessen P

GJB2 (gap junction protein beta 2)

Atlas Genet Cytogenet Oncol Haematol. 2003-05-01

Online version: http://atlasgeneticsoncology.org/gene/40716/gjb2