IGHMBP2 (immunoglobulin mu DNA binding protein 2)

2003-12-01  

Identity

HGNC
LOCATION
11q13.3
LOCUSID
ALIAS
CATF1,CMT2S,HCSA,HMN6,SMARD1,SMUBP2,ZFAND7
FUSION GENES

Other Information

Locus ID:

NCBI: 3508
MIM: 600502
HGNC: 5542
Ensembl: ENSG00000132740

Variants:

dbSNP: 3508
ClinVar: 3508
TCGA: ENSG00000132740
COSMIC: IGHMBP2

RNA/Proteins

Gene IDTranscript IDUniprot
ENSG00000132740ENST00000255078P38935
ENSG00000132740ENST00000539224F5GX64
ENSG00000132740ENST00000544541F5H5K3
ENSG00000132740ENST00000545146H3BRR1

Expression (GTEx)

0
5
10
15
20
25
30
35
40
45
50

References

Pubmed IDYearTitleCitations
383686102024RNA helicase IGHMBP2 regulates THO complex to ensure cellular mRNA homeostasis.2
388032252024IGHMBP2 deletion suppresses translation and activates the integrated stress response.0
383686102024RNA helicase IGHMBP2 regulates THO complex to ensure cellular mRNA homeostasis.2
388032252024IGHMBP2 deletion suppresses translation and activates the integrated stress response.0
346681232022Charcot-Marie-Tooth disease type 2S: identical novel missense mutation of IGHMBP2 gene in two unrelated families.1
356600622022Clinical and genetic features of Charcot-Marie-Tooth disease patients with IGHMBP2 mutations.3
360773112022Validation of the Pathogenic Effect of IGHMBP2 Gene Mutations Based on Yeast S. cerevisiae Model.3
346681232022Charcot-Marie-Tooth disease type 2S: identical novel missense mutation of IGHMBP2 gene in two unrelated families.1
356600622022Clinical and genetic features of Charcot-Marie-Tooth disease patients with IGHMBP2 mutations.3
360773112022Validation of the Pathogenic Effect of IGHMBP2 Gene Mutations Based on Yeast S. cerevisiae Model.3
295750952019Spinal muscular atrophy with respiratory distress type 1 associated with novel compound heterozygous mutations in IGHMBP2: Differential diagnosis in a case with congenital diaphragm eventration.1
295750952019Spinal muscular atrophy with respiratory distress type 1 associated with novel compound heterozygous mutations in IGHMBP2: Differential diagnosis in a case with congenital diaphragm eventration.1
302180342018UPF1-like helicase grip on nucleic acids dictates processivity.28
302180342018UPF1-like helicase grip on nucleic acids dictates processivity.28
280656842017IGHMBP2-related clinical and genetic features in a cohort of Chinese Charcot-Marie-Tooth disease type 2 patients.8

Citation

Dessen P

IGHMBP2 (immunoglobulin mu DNA binding protein 2)

Atlas Genet Cytogenet Oncol Haematol. 2003-12-01

Online version: http://atlasgeneticsoncology.org/gene/40935/ighmbp2